Congenital nasopharyngeal teratoma (epignathus) with airway obstruction

Authors

1 Assistant Professor of Pathology, Department of Pathology, Imam Khomeini Hospital, School of Medicine, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran

2 Resident of Pathology, Department Of Pathology, Imam Khomeini Hospital, School of Medicine, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran.

Abstract

Introduction: Teratomas of the nasopharynx are rare in neonates, usually presenting in the neonatal period with frequency of the total 1 in 4000 live birth and derived from the upper jaw, palate and sphenoid bone. It usually protrudes through the mouth, leading to obstruction of the upper airway .Teratoma of the head and neck are most-ly benign neoplasm. In this article we are reporting a case of Epignathus associated with airway obstruction.
Case report: A 40 day old male neonate was admitted with severe respiratory distress and nasopharyngeal mass protrude to the oral cavity prevented oral feeding. History of mild hydroaminious was positive. No other abnormali-ties were noted on physical examination. MRI of the head and neck revealed solid cystic mass with nasopharyngeal origin without intracranial extension. Mass was resected surgically and pathology revealed a mature teratoma dom-inantly composed of mature neuroglial elements and choroid plexus. Nasopharyngeal teratoma cases are interesting because of their obscure origin and unusual clinical presentation.surgical resection is the treatment of choice and should be done urgently in the case of airway ob-struction.

Highlights

Nastaran Ranjbari (PubMed)(Google Scholar)

Anahita Doustkhah Vajari (PubMed)(Google Scholar)

Keywords

References

1. He J, Wang Y, Zhu H, Qiu W, He Y. Nasopharyngeal ter-atoma associated with cleft palate in newborn. . 2010;(2):211-6.
2. Altuntaş EE, Bebek AI, Atalar M, Büyükkayhan D, Yasar M, Elagoz S.Nasopharyngeal teratoma causing airway obstruction in the neonate.BMJ . 2009;2009.
3. Hossein A, Mohammad A. Huge teratoma of the naso-pharynx. . 2007;:177–9.
4. Celik M, Akkaya H, Arda IS, Hicsonmez A. Congenital teratoma of the tongue: A case report and review of the literature. 2006;:25–8.
5. Sarin YK. An unusual congenital nasopharyngeal tera-toma. 1999;:56–7.
6. Ozturk A, Gunay GK, Akin MA, Arsalan F, Tekelioqlu F, Coban D. Multiple intraoral teratoma in anewborn in-fant. . 2012;(4):210-6.
7. Maartens IA, Wassenberg T, Halbertsma FJ, Marres HA,Andriessen P.Neonatal airway obstruction caused by rapidly growing nasopharyngeal . 2009;(11):1852-4.
8. Cukurova I, Gumussoy M, Yaz A, Bayol U, Yigitbasi OG.A benign teratoma presenting as an obstruction of the nasal cavity .. 2012;(1):147.
9. Som PM, Curtin HD: Head and Neck Imaging. 4th edi-tion. Mosby, St. , 2003:361.
10. Myers E, Suen J, Myers J, Hanna E: Cancer of the head and neck. In Cancer of the Head and Neck in the Pedi-atric Population. 4th edition. Edited by Whittemore K, Cunningham M. Saunders, Philadelphia; 2003:545-581.
11. De Bree R, Haasnoot K, Mahieu HF. Teratoma in a new-born: An unusual cause of airway obstruction. 1998;:39–42.
12. Demajumdar R, Epignathus Bhat N. A germ-cell tu-mour presenting as neonatal respiratory distress. 1999;:87–90.
13. Mirshemirani A, Khaleghnejad A, Mohajerzadeh L, Samsami M, Hasas -yeganeh S. Congenital nasopharyn-geal teratoma in a neonate. . 2011;(2):249-252.
14. Andronikou S, Kumbla S, Michelle Fink A. Neonatal na-sopharyngeal teratoma: Cross sectional imaging fea-tures. . 2003;(4):241–6.

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History

  • Receive Date: 19 April 2014
  • Revise Date: 11 October 2014
  • Accept Date: 23 November 2014

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